Ciliated hepatic foregut cyst (CHFC) is a rare foregut developmental malformation usually diagnosed in adulthood; however, rare cases have been reported in the pediatric population. CHFC can transform into a squamous cell carcinoma resulting in death despite surgical resection of the isolated malignancy. We report the presentation, evaluation, and surgical management of a symptomatic 17-year-old girl found to have a 6.5 × 4.5 cm CHFC and suggest that all patients with suspected CHFC undergo prompt evaluation and complete cyst excision.
Hepatic cyst excision Liver cyst Pediatric surgery Ciliated cyst
We would like to thank Aaron Shaver, MD (Department of Pathology) for providing the histopathology photographs. This study was supported in part by the National Research Service Award T32HS013833 (VZ) from the Agency of Healthcare Research and Quality, and by the National Institute of Diabetes and Digestive and Kidney Disease Training Grant 2T32DK007673-13 (MR); both from the National Institutes of Health and US Department of Health and Human Services.
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