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A novel association of duodenal atresia, malrotation, segmental dilatation of the colon, and anorectal malformation

  • Nobuyuki MorikawaEmail author
  • Tatsuo Kuroda
  • Toshiro Honna
  • Yoshihiro Kitano
  • Hideaki Tanaka
  • Hajime Takayasu
  • Akihiro Fijino
  • Noriko Kawashima
  • Hiroko Tanemura
  • Mitsuru Muto
  • Kentaro Matsuoka
Case Report

Abstract

We describe two female neonates who suffered from four gastrointestinal anomalies, including duodenal stenosis or atresia, malrotation, segmental dilatation of the colon, and anorectal malformation. Each patient was managed by two or three operations, resulting in good bowel movements. Since this is the first report of four gastrointestinal anomalies, these cases may provide clues to elucidate the etiology of gastrointestinal tract developmental abnormalities.

Keywords

Duodenal atresia Malrotation Segmental dilatation of the colon Anorectal malformation Sonic hedgehog 

Notes

Acknowledgments

The authors thank Paul D. Danielson, MD for reading the manuscript and helpful discussions.

Conflict of interest statement

There is no potential conflict of interest, and neither grants nor other form of payments were given to any authors.

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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Nobuyuki Morikawa
    • 1
    Email author
  • Tatsuo Kuroda
    • 1
  • Toshiro Honna
    • 1
  • Yoshihiro Kitano
    • 1
  • Hideaki Tanaka
    • 1
  • Hajime Takayasu
    • 1
  • Akihiro Fijino
    • 1
  • Noriko Kawashima
    • 1
  • Hiroko Tanemura
    • 1
  • Mitsuru Muto
    • 1
  • Kentaro Matsuoka
    • 2
  1. 1.Division of General SurgeryNational Center for Child Health and DevelopmentTokyoJapan
  2. 2.Division of PathologyNational Center for Child Health and DevelopmentTokyoJapan

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