Pediatric Surgery International

, Volume 24, Issue 8, pp 953–955 | Cite as

Dumbbell-shaped Ewing’s sarcoma family of tumor of thoracic spine in a child

  • Shuichiro Uehara
  • Takaharu Oue
  • Akihiro Yoneda
  • Yoshiko Hashii
  • Hideaki Ohta
  • Masahiro Fukuzawa
Case Report

Abstract

An 8-year-old boy was referred due to difficulty in walking. T1-weighted MRI detected a well-marginated lesion expanding from the epidural region in the spinal canal to the paravertebral area through the Th9 and Th10 intervertebral foramen. The patient underwent a biopsy under video-assisted thoracoscopy and the tumor was diagnosed as Ewing’s sarcoma family of tumor (ESFT). Imaging confirmed that the tumor completely disappeared and his neurologic functions were recovered perfectly at the end of treatment. Very few cases of skeletal ESFT of epidural extension in childhood have been documented. Video-assisted thoracoscopic surgery remains the best option for the diagnosis of endothoracic tumors in children.

Keywords

Ewing’s sarcoma family of tumor (ESFT) Dumbbell-shaped Video-assisted thoracoscopic surgery (VATS) Biopsy EWS-FLI1 

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Copyright information

© Springer-Verlag 2008

Authors and Affiliations

  • Shuichiro Uehara
    • 1
  • Takaharu Oue
    • 1
  • Akihiro Yoneda
    • 1
  • Yoshiko Hashii
    • 2
  • Hideaki Ohta
    • 2
  • Masahiro Fukuzawa
    • 1
  1. 1.Department of Pediatric SurgeryOsaka University Graduate School of MedicineOsakaJapan
  2. 2.Department of PediatricsOsaka University Graduate School of MedicineOsakaJapan

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