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Pediatric Surgery International

, Volume 23, Issue 9, pp 915–917 | Cite as

Alveolar capillary dysplasia presenting as pneumothorax: a case report and review of literature

  • Pankaj G. Roy
  • Prerna Patel
  • Anitha Vayalakkad
  • Colene Bowker
  • Kokila Lakhoo
Case Report

Abstract

Alveolar capillary dysplasia, although rare, is a universally fatal form of persistent pulmonary hypertension of the newborn. We report a case of a newborn male baby who developed respiratory distress and pneumothorax 11 h after an uncomplicated delivery. He deteriorated despite full ventilatory support and extracorporeal membrane oxygenation (ECMO). Open lung biopsy provided a diagnosis of alveolar capillary dysplasia and decision was made to withdraw treatment.

Keywords

Alveolar capillary dysplasia Pneumothorax ECMO 

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Copyright information

© Springer-Verlag 2007

Authors and Affiliations

  • Pankaj G. Roy
    • 1
    • 2
  • Prerna Patel
    • 1
  • Anitha Vayalakkad
    • 1
  • Colene Bowker
    • 3
  • Kokila Lakhoo
    • 1
  1. 1.Department of Paediatric SurgeryJohn Radcliffe hospitalOxfordUK
  2. 2.OxfordUK
  3. 3.Department of PathologyJohn Radcliffe HospitalOxfordUSA

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