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Pediatric Surgery International

, Volume 23, Issue 6, pp 609–611 | Cite as

Staged resection for a ruptured hepatoblastoma: a 6-year follow-up

  • Mansoor Ahmed MadanurEmail author
  • Narendra Battula
  • Mark Davenport
  • Anil Dhawan
  • Mohamed Rela
Case Report

Abstract

Hepatoblastoma (HB) is a rare germ cell tumour of childhood usually presenting with progressive abdominal distention. However, presentation as acute abdomen is a rare occurrence and is secondary to spontaneous rupture. This presentation carries high mortality. To our knowledge, six cases of ruptured hepatoblastoma have previously been reported, although the long-term outcome has not been clear. We report a case of ruptured HB who was managed by initial control of haemorrhage by laparotomy followed by chemotherapy with high-risk hepatoblastoma protocol as per SIOPEL 2 (cisplatin, carboplatin and doxorubicin) and a staged hepatectomy 5 months later. Patient is currently disease free at 6-year follow-up. Staged hepatectomy after initial control of haemorrhage does not preclude a curative resection.

Keywords

Ruptured hepatoblastoma Initial control of haemorrhage Adjuvant chemotherapy Staged hepatectomy 

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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Mansoor Ahmed Madanur
    • 1
    Email author
  • Narendra Battula
    • 1
  • Mark Davenport
    • 1
  • Anil Dhawan
    • 1
  • Mohamed Rela
    • 1
  1. 1.Kings College HospitalLondonUK

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