Pediatric Surgery International

, Volume 21, Issue 10, pp 809–812

Lipoblastoma/lipoblastomatosis: a clinicopathologic study of 16 cases in Taiwan

  • Shih-Ming Jung
  • Pei-Yeh Chang
  • Chih-Cheng Luo
  • Chen-Sheng Huang
  • Jin-Yao Lai
  • Chuen Hsueh
Original article

Abstract

Lipoblastoma/lipoblastomatosis is an uncommon benign lipomatous tumor affecting mainly infants and children. It presents as a painless mass located frequently in upper and lower extremities. The present study was conducted to characterize the clinicopathologic features of lipoblastoma/lipoblastomatosis in a Chinese population. A retrospective survey of 16 cases of pathologically confirmed lipoblastoma/lipoblastomatosis from 1988 to 2002 was performed. The available clinical information and histological sections were reviewed. The study involved 10 males and 6 females ranging in age from 5 to 49 months (median, 11.5 months). The patients presented with mass involving neck (n=5), inguina (n=3), feet (n=2), arm (n=1), leg (n=1), thorax (n=1), mesentery (n=1), buttock (n=1), and presacral region(n=1). The lesions were removed surgically. Histologically, the majority (11/16) of primary tumors were of diffuse type. Follow-up ranging from 5 to 125 months was available in 13 patients. Four patients experienced a recurrence of tumors in the neck (n=2) and lower extremities (n=2) 11–84 months after operation. The most common site of involvement of lipoblastoma/lipoblastomatosis in our series was the neck. A follow-up period of more than 3 years is recommended for patients with this condition.

Keywords

Lipoblastoma Lipoblastomatosis Adipose tumor 

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Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  • Shih-Ming Jung
    • 1
  • Pei-Yeh Chang
    • 2
  • Chih-Cheng Luo
    • 2
  • Chen-Sheng Huang
    • 2
  • Jin-Yao Lai
    • 2
  • Chuen Hsueh
    • 1
  1. 1.Department of Pathology, Chang Gung Memorial Hospital, Chang Gung Children’s HospitalChang Gung UniversityTaoyuanTaiwan
  2. 2.Department of Pediatric SurgeryChang Gung Children’s HospitalTaoyuanTaiwan

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