Child’s Nervous System

, Volume 13, Issue 11–12, pp 622–625 | Cite as

Successful conservative management of Gorham disease of the skull base and cervical spine

  • J. R. Mawk
  • Sergei K. Obukhov
  • William D. Nichols
  • Thomas D. Wynne
  • J. Michael Odell
  • Steven M. Urman
CASE REPORT

Abstract

Gorham’s disease, also called massive osteolysis or vanishing bone disease, is an enigmatic condition caused by endothelial proliferation occurring in bone and soft tissue. Death is frequent when there is spinal or visceral involvement. We present a case of spinal and skull base Gorham’s disease that was reversed by radiation therapy administered while the spine was supported by a halo vest. The literature is reviewed.

Key words Gorham’s disease Osteolysis Spinal instability Skull base tumors Radiotherapy 

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Copyright information

© Springer-Verlag Berlin Heidelberg 1997

Authors and Affiliations

  • J. R. Mawk
    • 1
  • Sergei K. Obukhov
    • 1
  • William D. Nichols
    • 2
  • Thomas D. Wynne
    • 3
  • J. Michael Odell
    • 4
  • Steven M. Urman
    • 5
  1. 1.Department of Neurosurgery, Emanuel Hospital, Portland, OR 97210, USAUS
  2. 2.Department of Pediatrics, Emanuel Hospital, Portland, OR 97210, USAUS
  3. 3.Department of Radiation Oncology, Emanuel Hospital, Portland, OR 97210, USAUS
  4. 4.Department of Pathology, Emanuel Hospital, Portland, OR 97210, USAUS
  5. 5.Department of Diagnostic Radiology, Emanuel Hospital, Portland, OR 97210, USAUS

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