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Primary spinal atypical teratoid/rhabdoid tumour presenting with hematomyelia and subarachnoid haemorrhage—a case report

  • Rajesh Kumar Meena
  • Ramesh S. DoddamaniEmail author
  • Harshad Chipde
  • Swati Mahajan
  • Sarat P. Chandra
  • Dattaraj P. Sawarkar
Case Report

Abstract

Atypical teratoid/rhabdoid tumours (AT/RTs) are highly aggressive and uncommon malignant tumours of the central nervous system (CNS) affecting children younger than 3 years of age. Primary spinal cord involvement is an extremely rare presentation. AT/RTs show necrosis and haemorrhages on histopathology frequently. However, spinal atypical teratoid/rhabdoid tumour (AT/RT) with hematomyelia and spinal subarachnoid haemorrhage (SAH), as seen in our case, has never been reported in the literature in the paediatric age group. We report a case of primary spinal AT/RT in a 3-year-old male child presenting acutely with hematomyelia and spinal SAH and try to elucidate its pathophysiological basis.

Keywords

Atypical teratoid/rhabdoid Cervical Spine SAH Hematomyelia 

Notes

Compliance with ethical standards

Conflict of interest

No conflict of interest for this study.

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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2019

Authors and Affiliations

  • Rajesh Kumar Meena
    • 1
  • Ramesh S. Doddamani
    • 1
    Email author
  • Harshad Chipde
    • 1
  • Swati Mahajan
    • 2
  • Sarat P. Chandra
    • 1
  • Dattaraj P. Sawarkar
    • 1
  1. 1.Department of NeurosurgeryAll India Institute of Medical Sciences (AIIMS)New DelhiIndia
  2. 2.Department of PathologyAll India Institute of Medical Sciences (AIIMS)New DelhiIndia

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