Child's Nervous System

, Volume 35, Issue 5, pp 871–874 | Cite as

Multimodel MRI features of an intracranial juvenile Xanthogranuloma

  • Jingkai Su
  • Ni Chen
  • Qiang YueEmail author
  • Weina Wang
  • Simin Zhang
  • Xiaorui Su
Case Report


Juvenile xanthogranuloma (JXG) is a benign, self-limiting histiocytic disorder of infancy and early childhood, usually presented as a single or multiple cutaneous lesions. The central nervous system is rarely affected by JXG. There were only a few reports of intracranial JXG cases which described its features on MR spectroscopy (MRS) and diffusion-weighted imaging (DWI), but its features on susceptibility-weighted imaging (SWI) and perfusion-weighted imaging (PWI) have not been reported yet. Here, we reported an intracranial JXG case which underwent multimodal MRI examinations including DWI, SWI, and PWI. The multimodal MRI provided a thorough insight into this disease and we found that intense enhancement and high perfusion may be important clues for the diagnosis.


Xanthogranuloma, juvenile Magnetic resonance imaging Perfusion-weighted imaging Diffusion-weighted imaging Susceptibility-weighted imaging 


Compliance with ethical standards

Conflict of interest

We declare that we do not have any commercial or associative interest that represents a conflict of interest in connection with the work submitted.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2019

Authors and Affiliations

  • Jingkai Su
    • 1
  • Ni Chen
    • 1
  • Qiang Yue
    • 1
    Email author
  • Weina Wang
    • 1
  • Simin Zhang
    • 1
  • Xiaorui Su
    • 1
  1. 1.Department of RadiologyWest China Hospital of Sichuan UniversityChengduChina

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