Primary intracranial extraosseous Ewing’s sarcoma
Common sites of occurrence of extraosseous Ewing’s sarcoma include the soft tissues and bones of the lower extremity, 12 paravertebral, and retroperitoneal regions. Primary intracranial Ewing’s sarcoma/pPNET is usually intraparenchymal located 13 when supratentorially, and an extraaxial epidural tumor radiographically mimicking a meningioma is extremely rare.
A 20-year14 old male presented to the emergency department with a 1-day history of drowsiness, headache, and fever. Neurological exam15 ination revealed decreased muscle strength (4/5) in the left lower limb. Head computed tomography scan showed an epidural 16 space-occupying lesion in the right temporoparietal region, which was assumed to be a meningioma by radiographic criteria. However, the surgical specimen was diagnosed as Ewing’s sarcoma.
Primary intracranial extraosseous Ewing’s sarcoma is a rare condition that may mimic a meningioma on imaging. Physicians must be cognizant of this possibility, particularly in any young individual with a solitary contrast-enhancing dural-based lesion.
KeywordsCentral nervous system Brain neoplasm Ewing’s sarcoma Epidural Extraosseous Molecular analysis
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Conflict of interest
The authors declare that they have no conflict of interest.
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