Child's Nervous System

, Volume 35, Issue 3, pp 541–545 | Cite as

Primary intracranial extraosseous Ewing’s sarcoma

  • Amir Humza SohailEmail author
  • Mohammed Sachal
  • Muhammad Arslan Arif Maan
  • Muhammad Soban
  • Muhammad Salman Khan
  • Muhammad Ehsan Bari
Case Report



Common sites of occurrence of extraosseous Ewing’s sarcoma include the soft tissues and bones of the lower extremity, 12 paravertebral, and retroperitoneal regions. Primary intracranial Ewing’s sarcoma/pPNET is usually intraparenchymal located 13 when supratentorially, and an extraaxial epidural tumor radiographically mimicking a meningioma is extremely rare.

Case Presentation

A 20-year14 old male presented to the emergency department with a 1-day history of drowsiness, headache, and fever. Neurological exam15 ination revealed decreased muscle strength (4/5) in the left lower limb. Head computed tomography scan showed an epidural 16 space-occupying lesion in the right temporoparietal region, which was assumed to be a meningioma by radiographic criteria. However, the surgical specimen was diagnosed as Ewing’s sarcoma.


Primary intracranial extraosseous Ewing’s sarcoma is a rare condition that may mimic a meningioma on imaging. Physicians must be cognizant of this possibility, particularly in any young individual with a solitary contrast-enhancing dural-based lesion.


Central nervous system Brain neoplasm Ewing’s sarcoma Epidural Extraosseous Molecular analysis 


Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Medical CollegeAga Khan UniversityKarachiPakistan
  2. 2.King Edward Medical UniversityLahorePakistan
  3. 3.Department of RadiologyAga Khan UniversityKarachiPakistan
  4. 4.Department of NeurosurgeryAga Khan UniversityKarachiPakistan

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