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Child's Nervous System

, Volume 34, Issue 12, pp 2497–2501 | Cite as

Limited dorsal myeloschisis with no extradural stalk linking to a flat skin lesion: a case report

  • Akiko Hiraoka
  • Takato Morioka
  • Nobuya Murakami
  • Satoshi O. Suzuki
  • Masahiro Mizoguchi
Case Report
  • 97 Downloads

Abstract

Background

Limited dorsal myeloschisis (LDM) is characterized by a fibroneural stalk linking the skin lesion to the underlying spinal cord.

Case presentation 

A 7-month-old girl with a lumbosacral “cigarette-burn” flat skin lesion underwent untethering surgery. The intradural tethering stalk appeared to originate at the dural wall and join the cord with no extradural stalk linking to the skin lesion. Histological examination of the intradural stalk revealed glial fibrillary acidic protein-immunopositive neuroglial tissues in the fibrocollagenous band, which is the central histopathological feature of an LDM stalk.

Conclusion

It is conceivable that the LDM stalk in our patient was originally linked to the skin lesion and subsequently regressed and was replaced by mature adipose tissue. We should be mindful of possible variations in the morphological features of LDM.

Keywords

Glial fibrillary acidic protein Fibroneural stalk Untethering 

Notes

Acknowledgments

We thank Jane Charbonneau, DVM, from Edanz Group (www.edanzediting.com/ac) for editing a draft of this manuscript.

Funding information

This work was partly supported by the Research Foundation of Fukuoka Children’s Hospital.

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Pediatric NeurologyFukuoka Children’s HospitalFukuokaJapan
  2. 2.Department of NeurosurgeryFukuoka Children’s HospitalFukuokaJapan
  3. 3.Department of Neuropathology, Graduate School of Medical SciencesKyushu UniversityFukuokaJapan
  4. 4.Department of NeurosurgeryKitakyushu Municipal Medical CenterKitakyushuJapan

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