Child's Nervous System

, Volume 33, Issue 3, pp 541–545 | Cite as

Surgical resection of large encephalocele: a report of two cases and consideration of resectability based on developmental morphology

  • Hideo OhbaEmail author
  • Satoshi Yamaguchi
  • Takashi Sadatomo
  • Masaaki Takeda
  • Manish Kolakshyapati
  • Kaoru Kurisu
Case Report



The first-line treatment of encephalocele is reduction of herniated structures. Large irreducible encephalocele entails resection of the lesion. In such case, it is essential to ascertain preoperatively if the herniated structure encloses critical venous drainage.

Case reports

Two cases of encephalocele presenting with large occipital mass underwent magnetic resonance (MR) imaging. In first case, the skin mass enclosed the broad space containing cerebrospinal fluid and a part of occipital lobe and cerebellum. The second case had occipital mass harboring a large portion of cerebrum enclosing dilated ventricular space. Both cases had common venous anomalies such as split superior sagittal sinus and high-positioned torcular herophili. They underwent resection of encephalocele without subsequent venous congestion. We could explain the pattern of venous anomalies in encephalocele based on normal developmental theory.


Developmental theory connotes that major dural sinuses cannot herniate into the sac of encephalocele. Irrespective to its size, encephalocele can be resected safely at the neck without subsequent venous congestion.


Encephalocele Neural tube defect Abnormal venous system Dural sinus Magnetic resonance imaging Developmental morphology 


Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest with regard to this study.


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Copyright information

© Springer-Verlag Berlin Heidelberg 2016

Authors and Affiliations

  • Hideo Ohba
    • 1
    Email author
  • Satoshi Yamaguchi
    • 1
  • Takashi Sadatomo
    • 2
  • Masaaki Takeda
    • 1
  • Manish Kolakshyapati
    • 1
  • Kaoru Kurisu
    • 1
  1. 1.Department of NeurosurgeryHiroshima University Graduate School of Biomedical and Health SciencesHiroshimaJapan
  2. 2.Department of NeurosurgeryNational Hospital Organization Higashihiroshima Medical CenterHigashihiroshimaJapan

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