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Child's Nervous System

, Volume 30, Issue 3, pp 527–530 | Cite as

The nature of double concomitant myxopapillary ependymoma: report of a case

  • J. Francisco SalomãoEmail author
  • Cecília Vianna de Andrade
  • Antonio Rosa Bellas
  • Tatiana Protzenko Cervante
Case Report

Abstract

Myxopapillary ependymomas are almost exclusively seen at the conus medullaris/filum terminale/cauda equina region, usually as solitary space-occupying lesions. The authors report the case of a 14-year-old boy with double concomitant myxopapillary ependymoma, proximal and caudal on the filum terminale in which a totally gross removal was achieved in two stages. This presentation is rare and, so far, we have known just three similar cases that were previously reported in children. The true nature of these lesions is controversial, and while some argue that they are related to metastatic seeding, others consider them independent lesions developing synchronously. A review on dissemination of spinal myxopapillary ependymomas was done.

Keywords

Myxopapillary ependymoma Spinal tumor Dissemination Drop metastasis Filum terminale 

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Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • J. Francisco Salomão
    • 1
    Email author
  • Cecília Vianna de Andrade
    • 2
  • Antonio Rosa Bellas
    • 1
  • Tatiana Protzenko Cervante
    • 1
  1. 1.Section of Pediatric Neurosurgery, Department of Pediatric Surgery, Fernandes Figueira National Institute for Health of Woman, Child and AdolescentOswaldo Cruz Foundation (IFF-Fiocruz)Rio de JaneiroBrazil
  2. 2.Department of Pathology, Fernandes Figueira National Institute for Health of Woman, Child and AdolescentOswaldo Cruz Foundation (IFF-Fiocruz)Rio de JaneiroBrazil

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