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Child's Nervous System

, Volume 28, Issue 4, pp 575–578 | Cite as

Management of pediatric patients with pseudotumor cerebri

  • Joshua J. ChernEmail author
  • R. Shane Tubbs
  • Amber S. Gordon
  • Katherine J. Donnithorne
  • W. Jerry Oakes
Original Paper

Abstract

Introduction

The care of patients with pseudotumor cerebri (idiopathic intracranial hypertension) involves ophthalmologists, neurologists and neurosurgeons. Its clinical characteristics in the pediatric population are distinct from those in adult patients.

Patients and methods

Fifty-nine patients diagnosed with pseudotumor cerebri were identified from the neurosurgery and neurology databases at Children’s Hospital, Birmingham, AL, USA. Clinical data were collected from the ophthalmology, neurology and neurosurgery departments.

Results

The average age of patients at diagnosis was 11.4 years (range 3–17). The average opening pressure of lumbar puncture (LP) was 37 cm of water. Most of the patients responded well to therapeutic LPs and medical management. Neurosurgical interventions included intracranial pressure monitoring and shunt insertion in nine patients. In three patients who presented with acute visual decline, two recovered and one remains legally blind.

Conclusions

The care of patients with pseudotumor cerebri requires a multiple-disciplinary approach. Neurosurgical interventions are sometimes needed for diagnostic and treatment purpose. Prompt and accurate communication among specialists is necessary to ensure timely treatment and optimal outcomes.

Keywords

Pseudotumor cerebri Idiopathic intracranial hypertension Cerebrospinal fluid Lumbar puncture 

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Copyright information

© Springer-Verlag 2012

Authors and Affiliations

  • Joshua J. Chern
    • 1
    Email author
  • R. Shane Tubbs
    • 1
  • Amber S. Gordon
    • 1
  • Katherine J. Donnithorne
    • 1
  • W. Jerry Oakes
    • 1
  1. 1.Department of Pediatric NeurosurgeryChildren’s HospitalBirminghamUSA

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