Child's Nervous System

, Volume 27, Issue 4, pp 517–521 | Cite as

Melanotic medulloblastoma in children

Case-Based Update

Abstract

Purpose

We report a case of melanotic medulloblastoma in a child. Reviewing the literature, we discuss the characteristics, therapeutic method, and prognosis of melanotic medulloblastoma in children.

Materials and methods

A 2-year-old girl was admitted with a mass located in the pineal region and presented obstructive hydrocephalus. The mass was subtotally resected through a slit-corpus–fornix approach. Thereafter, intraoperative direct third ventriculostomy was performed. The histopathological diagnosis of the mass suggested melanotic medulloblastoma.

Results

The MRI done at 4 days after surgery showed that the lateral ventricle normalized and the hydrocephalus was resolved. Thereafter, the patient underwent a Gamma Knife. The patient recovered well during the 8-month follow-up.

Conclusions

Melanotic medulloblastoma is a malignant tumor of childhood. It usually occurs at young age and might involve the vermis cerebelli, the fourth ventricle, and the pineal region. Surgery combined with radiotherapy and chemotherapy is recommended for children. But, it still requires observation to determine their long-term prognosis.

Keywords

Melanotic medulloblastoma Pineal region Child Tumor 

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Copyright information

© Springer-Verlag 2011

Authors and Affiliations

  • Wen-yan Li
    • 1
  • Lu Ma
    • 2
  • Jian Liu
    • 1
  • Hua Yang
    • 1
  • Qing Mao
    • 2
  1. 1.Department of NeurosurgeryAffiliated Hospital of Guiyang Medical CollegeGuiyangPeople’s Republic of China
  2. 2.Department of Neurosurgery, West China HospitalSichuan UniversityChengduPeople’s Republic of China

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