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Child's Nervous System

, 25:1455 | Cite as

Transsphenoidal meningoencephalocele associated with cleft lip and palate: challenges for diagnosis and surgical treatment

  • Diogo Franco
  • Nivaldo Alonso
  • Renata Ruas
  • Renato da Silva Freitas
  • Talita Franco
Original Paper

Abstract

Purpose

The aim of this study was to highlight the challenges for early diagnosis and the difficulties observed in surgical treatment of patients with transsphenoidal meningoencephalocele associated with cleft lip and/or palate.

Method

We evaluated six male patients treated over the course of 4 years. Five patients presented encephalic herniation with nonfunctional brain tissue; one of these presented herniation of the pituitary gland and cerebral ventricles.

Results

All the patients received surgical treatment for the cleft lip and/or palate. Only one patient underwent repair of the meningoencephalocele, via nasal endoscopy. There were no postprocedural clinical or surgical complications.

Conclusion

The tendency is to avoid neurosurgery, opting for periodic follow-up with magnetic resonance imaging. In the presence of cleft palate, palatoplasty is essential to protect the meningoencephalocele.

Keywords

Meningocele—diagnosis Meningocele—surgery Encephalocele—diagnosis Encephalocele—surgery Transsphenoidal encephalocele 

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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Diogo Franco
    • 1
  • Nivaldo Alonso
    • 2
  • Renata Ruas
    • 1
  • Renato da Silva Freitas
    • 3
  • Talita Franco
    • 1
  1. 1.UFRJRio de JaneiroBrazil
  2. 2.USPSão PauloBrazil
  3. 3.UFPRCuritibaBrazil

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