Child's Nervous System

, 24:1165 | Cite as

Specific entities affecting the craniocervical region: Down’s syndrome

Special Annual Issue
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Abstract

Introduction

The ligamentous laxities and bony abnormalities associated with Down’s syndrome, os odontoideum, achondroplasia, osteogenesis imperfecta, and basilar invagination have been discussed with the imaging of the craniocervical junction. These are significant and require suspicion when dealing with children with the previously mentioned entities.

Conclusion

Previous adverse surgical results in managing these patients reflect the lack of understanding of the underlying pathology and the appropriate surgical treatment.

Keywords

Down’s syndrome Os odontoideum Achondroplasia Osteogenesis imperfecta Basilar invagination Bony abnormalities 
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Copyright information

© Springer-Verlag 2008

Authors and Affiliations

  1. 1.Department of NeurosurgeryUniversity of Iowa Hospitals and ClinicsIowa CityUSA

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