Child's Nervous System

, Volume 23, Issue 10, pp 1103–1109 | Cite as

Pansynostosis: a review

  • Jeffrey P. Blount
  • Robert G. LouisJr.
  • R. Shane Tubbs
  • John H. Grant
Review Paper

Abstract

Introduction

Although rare, pansynostoses are seen and treated by the craniofacial surgeon. To date, a single source that reviews these more severe forms of craniosynostosis is lacking in the literature.

Materials and methods

The present paper outlines and reviews the associations of both syndromic and nonsyndromic cases, potential mechanisms, and the anatomy involved with such forms of premature fusion of the cranial sutures.

Results

Pansynostosis is seen in a myriad of syndromes but can also be identified in nonsyndromic cases. Raised intracranial pressure is a concern in these patients.

Conclusions

Early recognition and treatment of patients with pansynostosis of the cranial sutures is important.

Keywords

Skull Craniosynostosis Premature fusion Multisutural 

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Copyright information

© Springer-Verlag 2007

Authors and Affiliations

  • Jeffrey P. Blount
    • 1
  • Robert G. LouisJr.
    • 1
  • R. Shane Tubbs
    • 1
    • 3
  • John H. Grant
    • 2
  1. 1.Division of NeurosurgeryUniversity of Alabama at BirminghamBirminghamUSA
  2. 2.Division of Plastic SurgeryUniversity of Alabama at BirminghamBirminghamUSA
  3. 3.Pediatric NeurosurgeryChildren’s HospitalBirminghamUSA

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