Child's Nervous System

, Volume 20, Issue 5, pp 323–328

History, anatomic forms, and pathogenesis of Chiari I malformations

Focus Session



Chiari I malformations constitute a group of entities of congenital or acquired etiology that have in common descent of the cerebellar tonsils into the cervical spinal canal. In recent years, since the advent of magnetic resonance imaging, an increasing number of asymptomatic, doubtfully symptomatic, and minimally symptomatic patients with Chiari I malformations have been diagnosed. This has resulted in controversy about the multiple therapeutic strategies indicated for these problems.


With the intention of updating the knowledge that we currently have on the Chiari I malformation and the related syringomyelia we review the literature and discuss the historical background, pathogenesis, anatomic forms, clinical presentation, and diagnostic procedures of these abnormalities.


Chiari I malformation Foramen magnum decompression Hydromyelia Posterior fossa decompression Syringomyelia 


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Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  1. 1.Section of NeurosurgeryHospital C. DurandBuenos AiresArgentina
  2. 2.Division of NeurosurgeryUniversity of Buenos Aires School of MedicineBuenos AiresArgentina

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