Child's Nervous System

, Volume 20, Issue 2, pp 100–103 | Cite as

Familial posterior fossa arachnoid cyst

Original Paper



Arachnoid cysts are a relatively common incidental finding on CT scans of the brain. They most commonly occur in the middle cranial fossa, where familial occurrence has rarely been reported. Posterior fossa arachnoid cysts are more unusual.

Case histories

We report the presence of quadrigeminal cistern arachnoid cysts in siblings.


Arachnoid cyst Familial obstructive hydrocephalus management 


  1. 1.
    Allen A, Wiegmann TB, MacDougall ML (1986) Arachnoid cyst in a patient with autosomal-dominant polycystic kidney disease. Am J Kidney Dis 8:128–130PubMedGoogle Scholar
  2. 2.
    Go KG, Houthoff HJ, Blaauw EH, Havinga P, Hartsuiker J (1984) Arachnoid cysts of the sylvian fissure. Evidence of fluid secretion. J Neurosurg 60:803–813PubMedGoogle Scholar
  3. 3.
    Hald JK, Nakstad PH, Skjeldal OH, Stromme P (1991) Bilateral arachnoid cysts of the temporal fossa in four children with glutaric aciduria type I. AJNR Am J Neuroradiol 12:407–409PubMedGoogle Scholar
  4. 4.
    Handa J, Okamoto K, Sato M (1981) Arachnoid cyst of the middle cranial fossa: report of bilateral cysts in siblings. Surg Neurol 16:127–130PubMedGoogle Scholar
  5. 5.
    Jamjoom ZA, Okamoto E, Jamjoom AH, al-Hajery O, Abu-Melha A (1995) Bilateral arachnoid cysts of the sylvian region in female siblings with glutaric aciduria type I. Report of two cases. J Neurosurg 82:1078–1081PubMedGoogle Scholar
  6. 6.
    Lutcherath V, Waaler PE, Jellum E, Wester K (2000) Children with bilateral temporal arachnoid cysts may have glutaric aciduria type 1 (GAT1); operation without knowing that may be harmful. Acta Neurochir (Wien) 142:1025–1030Google Scholar
  7. 7.
    Martinez-Lage JF, Casas C, Fernandez MA, Puche A, Rodriguez Costa T, Poza M (1994) Macrocephaly, dystonia, and bilateral temporal arachnoid cysts: glutaric aciduria type 1. Childs Nerv Syst 10:198–203PubMedGoogle Scholar
  8. 8.
    Masuno M, Fukushima Y, Sugio Y, Kuroki Y (1987) Partial distal 12q trisomy with arachnoid cyst. Jinrui Idengaku Zasshi 32:39–43PubMedGoogle Scholar
  9. 9.
    Pomeranz S, Constantini S, Lubetzki-Korn I, Amir N (1991) Familial intracranial arachnoid cysts (review). Childs Nerv Syst 7:100–102PubMedGoogle Scholar
  10. 10.
    Rengachary SS, Watanabe I (1981) Ultrastructure and pathogenesis of intracranial arachnoid cysts. J Neuropathol Exp Neurol 40:61–83Google Scholar
  11. 11.
    Renner C, Razeghi S, Uberall MA, Hartmann P, Lehnert W (1997) Clinically asymptomatic glutaric aciduria type I in a 4 5/12-year-old girl with bilateral temporal arachnoid cysts. J Inherit Metab Dis 20:840–841CrossRefPubMedGoogle Scholar
  12. 12.
    Tolmie JL, Day R, Fredericks B, Galea P, Moffett AW (1997) Dominantly inherited cerebral dysplasia: arachnoid cyst associated with mild mental handicap in a mother and her son. J Med Genet 34:1018–1020PubMedGoogle Scholar
  13. 13.
    Wester K (1999) Peculiarities of intracranial arachnoid cysts: location, sidedness, and sex distribution in 126 consecutive patients. Neurosurgery 45:775–779PubMedGoogle Scholar

Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  1. 1.Department of Neurosurgery, Institute of NeurosciencesSouthern General HospitalGlasgowUK
  2. 2.Department of NeurosurgeryHull Royal InfirmaryHullUK

Personalised recommendations