Heart and Vessels

, Volume 32, Issue 2, pp 234–239 | Cite as

Interventricular dyssynchrony in a patient with a biventricular physiology and a systemic right ventricle

  • Aya MiyazakiEmail author
  • Heima Sakaguchi
  • Kanae Noritake
  • Yosuke Hayama
  • Jun Negishi
  • Koji Kagisaki
  • Kenji Yasuda
  • Hajime Ichikawa
  • Hideo Ohuchi
Case Report


We describe of a unique pattern of cardiac dyssynchrony in a patient with a biventricular physiology and systemic right ventricle (RV): the interventricular dyssynchrony due to a contraction delay between the left ventricle and RV. In the present case, the cineangiography and intracardiac electrocardiography of the RV did not reveal intraventricular dyssynchrony of the RV, but revealed interventricular dyssynchrony. In addition, the pressure curves of the ventricles exhibited time phase differences between the two ventricles. The cardiac resynchronization therapy determining the pacing lead positions based on the idea of interventricular dyssynchrony induced reverse cardiac remodeling in this patient with systemic RV dysfunction.


Congenital heart disease Systemic right ventricle Interventricular dyssynchrony Cardiac resynchronization therapy Atrioventricular discordance 



The authors wish to express their gratitude to Mr. John Martin for his assistance in preparing the manuscript.

Compliance with ethical standards

Ethical standards

All procedures contributing to this work were performed under given the informed consent, and were complied with the ethical standards of the relevant national guidelines on human experimentation (Japan) and with the Helsinki Declaration of 1975 (as revised in 2008). Also this study was approved by the institutional ethics committees (M25-021). The authors have no financial conflicts of interest to disclose concerning this study.

Supplementary material

Supplementary file 1A. The anteroposterior view of the right ventriculography before the cardiac resynchronization therapy (MPG 2675 kb)

Supplementary file 1B. The lateral view of the right ventriculography before the cardiac resynchronization therapy (MPG 2675 kb)

Supplementary file 2A. The anteroposterior view of the right ventriculography 6 months after the cardiac resynchronization therapy (MPG 2996 kb)

Supplementary file 2B. The lateral view of the right ventriculography 6 months after the cardiac resynchronization therapy (MPG 2996 kb)


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Copyright information

© Springer Japan 2016

Authors and Affiliations

  • Aya Miyazaki
    • 1
    Email author
  • Heima Sakaguchi
    • 1
  • Kanae Noritake
    • 1
  • Yosuke Hayama
    • 1
  • Jun Negishi
    • 1
  • Koji Kagisaki
    • 2
  • Kenji Yasuda
    • 3
  • Hajime Ichikawa
    • 2
  • Hideo Ohuchi
    • 1
  1. 1.Department of Pediatric CardiologyNational Cerebral and Cardiovascular CenterSuitaJapan
  2. 2.Department of Pediatric Cardiovascular SurgeryNational Cerebral and Cardiovascular CenterSuitaJapan
  3. 3.Department of PediatricsShimane University School of MedicineMatsueJapan

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