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Heart and Vessels

, Volume 22, Issue 4, pp 278–283 | Cite as

Intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism in a patient with Behçet's disease: a case report and literature review

  • Takashi Kajiya
  • Ryuichiro AnanEmail author
  • Masahiro Kameko
  • Naoko Mizukami
  • Shinichi Minagoe
  • Shuichi Hamasaki
  • Ikuro Maruyama
  • Ryuzo Sakata
  • Chuwa Tei
CASE REPORT

Abstract

A 26-year-old woman with intermittent fever was admitted to our hospital, and gradually developed facial edema. Examinations including computed tomography, transesophageal echocardiography, digital subtraction angiography, and pulmonary perfusion scintigraphy revealed intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism. Clinical findings and laboratory data led us to make a diagnosis of Behçet's disease. Combination of intracardiac thrombus, superior vena cava syndrome, and pulmonary embolism are rare complications in Behçet's disease. Behçet's disease should be considered in the differential diagnosis of intracardiac mass of the right heart, and early diagnosis and treatment are essential for the management of Behçet's disease especially with large-vessel manifestations. In addition to a case report, we review the literature and report the characteristics of intracardiac thrombus in Behçet's disease.

Key words

Behçet's disease Intracardiac thrombus Superior vena cava syndrome Pulmonary embolism 

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Copyright information

© Springer-Verlag Tokyo 2007

Authors and Affiliations

  • Takashi Kajiya
    • 1
  • Ryuichiro Anan
    • 1
    Email author
  • Masahiro Kameko
    • 1
  • Naoko Mizukami
    • 2
  • Shinichi Minagoe
    • 1
  • Shuichi Hamasaki
    • 1
  • Ikuro Maruyama
    • 2
  • Ryuzo Sakata
    • 3
  • Chuwa Tei
    • 1
  1. 1.Department of Cardiovascular, Respiratory and Metabolic MedicineGraduate School of Medicine, Kagoshima UniversityKagoshimaJapan
  2. 2.Department of Laboratory and Molecular MedicineGraduate School of Medicine, Kagoshima UniversityKagoshimaJapan
  3. 3.Department of Cardiovascular SurgeryGraduate School of Medicine, Kagoshima UniversityKagoshimaJapan

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