European Radiology

, Volume 13, Supplement 6, pp L147–L150 | Cite as

Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging

  • Ulrich KramerEmail author
  • Volker Dörnberger
  • Michael Fenchel
  • Norbert Stauder
  • Claus D. Claussen
  • Stephan Miller


Scimitar syndrome has a variable presentation depending on the age at which the diagnosis is made. We report a case of a young woman (age 18 years) with suspected right pulmonary hypoplasia in whom a scimitar syndrome was diagnosed. Using MRI morphological findings and hemodynamic significance of the syndrome were assessed. Left-to-right shunt was calculated from blood flow measurements performed in the ascending aorta, the main pulmonary artery, and the aberrant scimitar vein.


MR imaging Chest Congenital heart disease Scimitar syndrome 


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Copyright information

© Springer-Verlag 2003

Authors and Affiliations

  • Ulrich Kramer
    • 1
    Email author
  • Volker Dörnberger
    • 1
  • Michael Fenchel
    • 1
  • Norbert Stauder
    • 1
  • Claus D. Claussen
    • 1
  • Stephan Miller
    • 1
  1. 1.Department of Diagnostic RadiologyUniversity of TuebingenTuebingenGermany

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