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European Radiology

, Volume 13, Supplement 6, pp L147–L150 | Cite as

Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging

  • Ulrich KramerEmail author
  • Volker Dörnberger
  • Michael Fenchel
  • Norbert Stauder
  • Claus D. Claussen
  • Stephan Miller
Chest

Abstract

Scimitar syndrome has a variable presentation depending on the age at which the diagnosis is made. We report a case of a young woman (age 18 years) with suspected right pulmonary hypoplasia in whom a scimitar syndrome was diagnosed. Using MRI morphological findings and hemodynamic significance of the syndrome were assessed. Left-to-right shunt was calculated from blood flow measurements performed in the ascending aorta, the main pulmonary artery, and the aberrant scimitar vein.

Keywords

MR imaging Chest Congenital heart disease Scimitar syndrome 

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Copyright information

© Springer-Verlag 2003

Authors and Affiliations

  • Ulrich Kramer
    • 1
    Email author
  • Volker Dörnberger
    • 1
  • Michael Fenchel
    • 1
  • Norbert Stauder
    • 1
  • Claus D. Claussen
    • 1
  • Stephan Miller
    • 1
  1. 1.Department of Diagnostic RadiologyUniversity of TuebingenTuebingenGermany

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