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European Radiology

, Volume 12, Issue 10, pp 2542–2547 | Cite as

Unilateral cerebral polymicrogyria with ipsilateral cerebral hemiatrophy

  • Katsumi Hayakawa
  • Toyoko Kanda
  • Yuriko Yamori
Neuro

Abstract.

We evaluated six children in whom MR imaging showed unilateral cerebral polymicrogyria associated with ipsilateral cerebral atrophy and ipsilateral brain stem atrophy. The aim of this study was to clarify whether this disorder based on neuroimaging constitutes a new homogeneous clinical entity. The subjects were six children whose ages at the time of MR imaging ranged from 8 months to 11 years. Their clinical and MR features were analyzed. All of the children were born between 38 and 42 weeks gestation, without any significant perinatal events. Spastic hemiplegia and epilepsy were observed in all of the patients, and mental retardation was observed in four. The MR findings included unilateral cerebral polymicrogyria associated with ipsilateral cerebral hemiatrophy and ipsilateral brain stem atrophy in all patients. The ipsilateral sylvian fissure was hypoplastic in four patients. These patients showed relatively homogeneous clinical and neuroimaging features. Although the additional clinical features varied according to the site and the extent affected by the polymicrogyria, this disorder could constitute a new relatively homogeneous clinical entity.

Congenital hemiplegia Asymmetric polymicrogyria Cerebral hemiatrophy MR imaging Non-lissencephalic cortical dysplasia 

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Copyright information

© Springer-Verlag 2002

Authors and Affiliations

  • Katsumi Hayakawa
    • 1
  • Toyoko Kanda
    • 2
  • Yuriko Yamori
    • 2
  1. 1.Department of Radiology, Kyoto City Hospital, 1-2 Higashi-Takada-cho, Mibu, Nakagyo-ku, 604-8845 KyotoJapan
  2. 2.Department of Pediatric Neurology, St. Joseph Hospital for Handicapped Children, 603-8323 KyotoJapan

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