Rheumatology International

, Volume 33, Issue 4, pp 1093–1096 | Cite as

Acute myocarditis and ventricular fibrillation as initial presentation of pediatric systemic lupus erythematosus

  • Chi-Nan Huang
  • Hsin-Hui Yu
  • Shuenn-Nan Chiu
  • Jyh-Hong Lee
  • Li-Chieh Wang
  • Yao-Hsu Yang
  • Bor-Luen ChiangEmail author
Short Communication


Acute myocarditis and ventricular arrhythmia are rarely seen as the initial presentation of systemic lupus erythematosus (SLE) in children. We reported the case of a 12-year-old girl with congestive heart failure, acute myocarditis and pericardial effusion as a primary manifestation of SLE. Sudden cardiovascular collapse due to ventricular fibrillation (VF), ventricular tachycardia (VT) and cardiac tamponade occurred. After resuscitation and pericardiocentesis, frequent VF/VT refractory to anti-arrhythmic therapy was supported by venoarterial extracorporeal membrane oxygenation. Early diagnosis and a combination treatment for heart failure, arrhythmias and immunosuppression may result in a favorable outcome.


SLE Myocarditis Ventricular arrhythmia Extracorporeal membrane oxygenation 


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Copyright information

© Springer-Verlag 2011

Authors and Affiliations

  • Chi-Nan Huang
    • 1
  • Hsin-Hui Yu
    • 1
  • Shuenn-Nan Chiu
    • 1
  • Jyh-Hong Lee
    • 1
  • Li-Chieh Wang
    • 1
  • Yao-Hsu Yang
    • 1
  • Bor-Luen Chiang
    • 1
    Email author
  1. 1.Department of PediatricsNational Taiwan University HospitalTaipeiTaiwan

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