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Rheumatology International

, Volume 32, Issue 3, pp 607–610 | Cite as

Primary hypertrophic osteoarthropathy

  • Hadi Poormoghim
  • Aref Hosseynian
  • Aryan Javadi
Original Article

Abstract

Pachydermoperiostosis PDP (idiopathic or primary hypertrophic osteoarthropathy) is a rare congenital disease that inherited in an autosomal fashion. The disease is more common in males and develops gradually from adulthood. The disease is characterized by coarse facial features, clubbing of the fingers and radiographic periostitis of the distal long bones. The patient was a 37-year-old man with acroosteolysis and digital clubbing of hands and feet fingers and lion facies.

Keywords

Pachydermoperiostosis Primary hypertrophic osteoarthropathy Digital clubbing Acroosteolysis 

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Copyright information

© Springer-Verlag 2010

Authors and Affiliations

  • Hadi Poormoghim
    • 1
  • Aref Hosseynian
    • 1
  • Aryan Javadi
    • 1
  1. 1.F. Sodagari University of Medical Sciences and Health Care ServicesTehranIran

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