Rheumatology International

, Volume 31, Issue 1, pp 85–88 | Cite as

Acute pseudogout of the neck—the crowned dens syndrome: 2 case reports and review of the literature

  • Keith Siau
  • Martin Lee
  • Catherine J. LaversuchEmail author
Case Report


Acute pseudogout of the neck, also known as the crowned dens syndrome, is a rare cause of neck pain characterised by crystalline deposition in periodontoid articular tissues. It is typified clinically by severe cervical pain and stiffness, often in conjunction with pyrexia and raised inflammatory markers. As such, it is often misdiagnosed. We report 2 cases of crowned dens syndrome masquerading respectively as meningitis and polymyalgia rheumatica, and review the literature with particular attention to the clinical and radiological aspects of this under-recognised condition.


Pseudogout Crowned dens syndrome CDS 


Conflict of interest statement

The authors declare no conflicts of interest.


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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Keith Siau
    • 1
  • Martin Lee
    • 2
  • Catherine J. Laversuch
    • 1
    Email author
  1. 1.Department of RheumatologyMusgrove Park HospitalTauntonUK
  2. 2.Department of RheumatologyRoyal Cornwall HospitalTruroUK

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