Rheumatology International

, Volume 30, Issue 1, pp 105–107 | Cite as

Monckeberg’s sclerosis in a patient with systemic sclerosis

  • Chang-Nam Son
  • Kyong-Hee Jung
  • Soon-Young Song
  • Jae-Bum JunEmail author
Case Report


Monckeberg’s sclerosis (MS) is one of the non-inflammatory vascular diseases characterized by calcification of the media of small and medium-sized muscular arteries, but is distinct from atherosclerosis. We present a case of MS that was incidentally detected by plain X-ray in a patient with systemic sclerosis. We took CT angiographs of the patient’s lower extremities for the differential diagnosis of vascular calcification, which was confirmed. To determine if systemic sclerosis is a risk factor for MS, we reviewed plain X-rays from 43 well-documented systemic sclerosis patients, but we did not detect any cases of MS. We therefore conclude that systemic sclerosis may not be a risk factor for MS.


Systemic sclerosis Vascular calcification Monckeberg’s sclerosis 


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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Chang-Nam Son
    • 1
  • Kyong-Hee Jung
    • 1
  • Soon-Young Song
    • 1
  • Jae-Bum Jun
    • 1
    Email author
  1. 1.Hanyang UniversitySeoulKorea

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