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Rheumatology International

, Volume 29, Issue 2, pp 207–209 | Cite as

Bronchus-associated lymphoid tissue lymphoma in a patient with primary Sjögren’s syndrome

  • Francesca IngegnoliEmail author
  • Alba Sciascera
  • Valentina Galbiati
  • Vincenzo Corbelli
  • Enzo D’Ingianna
  • Flavio Fantini
Case Report

Abstract

Despite its infrequent occurrence, the possible development of lymphoma or lymphoid lung disease in patients with Sjögren’s syndrome should always be borne in mind. We describe a case of bronchus-associated lymphoid tissue (BALT) lymphoma in a patient with Sjögren’s syndrome that clearly exemplifies the wide-ranging problems of diagnosing, treating and following such patients. This difficulty is due to the fact that the clinical and radiological findings suggest interstitial lung disease, and histological assays are required for a correct diagnosis. A precise knowledge of the various histological and radiological patterns of lung involvement can aid patient management.

Keywords

Sjögren’s syndrome BALT lymphoma 

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Copyright information

© Springer-Verlag 2008

Authors and Affiliations

  • Francesca Ingegnoli
    • 1
    Email author
  • Alba Sciascera
    • 2
  • Valentina Galbiati
    • 1
  • Vincenzo Corbelli
    • 2
  • Enzo D’Ingianna
    • 2
  • Flavio Fantini
    • 1
  1. 1.Department of RheumatologyIstituto Gaetano Pini, Chair of Rheumatology, University of MilanMilanItaly
  2. 2.Department of Internal MedicineAzienda Ospedaliera S. AnnaComoItaly

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