Rheumatology International

, Volume 27, Issue 8, pp 767–770 | Cite as

Large pericardial effusion requiring pericardiocentesis as cardinal sign of macrophage activation syndrome in systemic onset-juvenile idiopathic arthritis

  • Donato Rigante
  • Gabriella  De Rosa
  • Barbara Bertoni
  • Valentina Ansuini
  • Manuela Pardeo
  • Ilaria La Torraca
  • Stefania Gaspari
  • Achille Stabile
Case Report


We report a case of large pericardial effusion which has been managed with pericardiocentesis as the main presentation feature of a dramatic clinical picture, only retrospectively framed as referred to macrophage activation syndrome in a child with juvenile idiopathic arthritis at its onset. The risk of developing this rare and severe complication should be recognized in various pathological settings of childhood, above all in children displaying systemic signs of juvenile idiopathic arthritis.


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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Donato Rigante
    • 1
  • Gabriella  De Rosa
    • 1
  • Barbara Bertoni
    • 1
  • Valentina Ansuini
    • 1
  • Manuela Pardeo
    • 1
  • Ilaria La Torraca
    • 1
  • Stefania Gaspari
    • 1
  • Achille Stabile
    • 1
  1. 1.Department of Pediatric SciencesUniversità Cattolica Sacro CuoreRomeItaly

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