Successful treatment of acquired amegakaryocytic thrombocytopenia with cyclosporine in adult onset Still’s disease
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Acquired amegakaryocytic thrombocytopenia (AAT) is a rare disorder, characterized by severe thrombocytopenia and selective, marked decrease or absence of megakaryocytes in the bone marrow. We describe a 29-year-old female with adult onset Still’s disease preceding a diagnosis of AAT and autoimmune hemolytic anemia, which was successfully treated with cyclosporine. This is the first case of AAT in a patient with adult onset Still’s disease.
KeywordsAcquired amegakaryocytic thrombocytopenia Autoimmune hemolytic anemia Adult-onset Still’s disease Cyclosporine
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