Rheumatology International

, Volume 27, Issue 3, pp 295–298 | Cite as

Successful treatment of acquired amegakaryocytic thrombocytopenia with cyclosporine in adult onset Still’s disease

  • Min-Young Her
  • Tae-Hwan Kim
  • Hyun-Kyu Chang
  • Woong-Soo Lee
  • Dae-Hyun Yoo
Case Report

Abstract

Acquired amegakaryocytic thrombocytopenia (AAT) is a rare disorder, characterized by severe thrombocytopenia and selective, marked decrease or absence of megakaryocytes in the bone marrow. We describe a 29-year-old female with adult onset Still’s disease preceding a diagnosis of AAT and autoimmune hemolytic anemia, which was successfully treated with cyclosporine. This is the first case of AAT in a patient with adult onset Still’s disease.

Keywords

Acquired amegakaryocytic thrombocytopenia Autoimmune hemolytic anemia Adult-onset Still’s disease Cyclosporine 

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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Min-Young Her
    • 1
    • 4
  • Tae-Hwan Kim
    • 1
  • Hyun-Kyu Chang
    • 2
  • Woong-Soo Lee
    • 3
  • Dae-Hyun Yoo
    • 1
  1. 1.Division of Rheumatology, The Hospital for Rheumatic DiseasesHanyang UniversitySeoulSouth Korea
  2. 2.Department of Internal MedicineDankook University Medical CollegeChonanSouth Korea
  3. 3.Department of Laboratory MedicineHanyang University Medical CollegeSeoulSouth Korea
  4. 4.Department of Internal MedicinePaik University Medical CollegeBusanSouth Korea

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