Rheumatology International

, Volume 24, Issue 5, pp 301–304 | Cite as

Allergic granulomatosis and angiitis in the absence of asthma and blood eosinophilia: a rare presentation of limited Churg-Strauss syndrome

  • Alper Sevinc
  • H. Canan Hasanoglu
  • Munire Gokirmak
  • Zeki Yildirim
  • Tamer Baysal
  • Bulent Mizrak
Case Report

Abstract

Allergic granulomatosis and angiitis, also known as Churg-Strauss syndrome (CSS), is an uncommon vasculitis of unknown etiology. We report a 21-year-old male patient with fatigue, dry cough, and progressive dyspnea. He had no history of asthma or eosinophilia. Thorax computed tomography showed bullous/cystic areas with thin walls in varying sizes (5–15 mm). Histopathological examination of the open lung biopsy revealed granulomatous infiltration with histiocytes and eosinophilic leukocytes. This extremely rare variant of CSS is discussed.

Keywords

Asthma Churg-Strauss syndrome Eosinophilia 

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Copyright information

© Springer-Verlag 2003

Authors and Affiliations

  • Alper Sevinc
    • 1
  • H. Canan Hasanoglu
    • 2
  • Munire Gokirmak
    • 3
  • Zeki Yildirim
    • 3
  • Tamer Baysal
    • 4
  • Bulent Mizrak
    • 5
  1. 1.Department of Internal Medicine, Gaziantep University School of MedicineSahinbey Medical CenterGaziantep 27310Turkey
  2. 2.Department of Chest DiseasesAtaturk Chest Diseases and Thoracic Surgery CenterAnkaraTurkey
  3. 3.Department of Chest Diseases, Inonu University School of MedicineTurgut Ozal Medical CenterMalatyaTurkey
  4. 4.Department of Radiology, Inonu University School of MedicineTurgut Ozal Medical CenterMalatyaTurkey
  5. 5.Department of Pathology, Inonu University School of MedicineTurgut Ozal Medical CenterMalatyaTurkey

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