Complete bilateral Tessier’s facial cleft number 5: surgical strategy for a rare case report

  • Aurélien BinetEmail author
  • A. de Buys Roessingh
  • M. Hamedani
  • O. El Ezzi
Original Article


The oro-ocular cleft number 5 according to the Tessier classification is one of the rarest facial clefts and few cases have been reported in the literature. Although the detailed structure of rare craniofacial clefts is well established, the cause of these pathological conditions is not. There are no existing guidelines for the management of this particular kind of cleft. We describe the case of a 19-month-old girl with a complete bilateral facial cleft. We describe the surgical steps taken to achieve the primary correction of the soft tissue deformation. Embryologic development and radiological approach are discussed, as are also the psychological and social aspects of severe facial deformities.


Orofacial cleft 5 Cleft palate Oblique facial cleft Craniofacial abnormalities 



The authors are grateful to Annette Wagnière for reviewing the English text.

Author contributions

AB, OEE, AdBR. data management, data analysis, manuscript writing, AB, OEE. data analysis, manuscript writing, OEE, MH. data management, data analysis, AdBR, OEE. project development, data collection.

Compliance with ethical standards

Conflict of interest

All the authors declare that they have no conflict of interest.


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© Springer-Verlag France SAS, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryCURCP, University Hospital Center of the Canton of Vaud (CHUV)LausanneSwitzerland
  2. 2.Department of Ophtalmology, Jules Gonin HospitalUniversity Hospital Center of the Canton of Vaud (CHUV)LausanneSwitzerland

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