CardioVascular and Interventional Radiology

, Volume 42, Issue 2, pp 308–312 | Cite as

Percutaneous Orthotopic IVC Construction in a Pediatric Patient with Symptomatic IVC Agenesis

  • Marc H. SchiffmanEmail author
  • Joshua Cornman-Homonoff
  • Thomas A. Sos
Case Report


Inferior vena cava agenesis is an uncommon condition usually attributed to embryologic dysgenesis. When symptomatic, unprovoked deep venous thrombosis and/or lower extremity venous congestion are the most frequent manifestations. Its rarity has precluded consensus regarding appropriate management. Symptomatic chronic venous congestion requires surgical construction of auxiliary venous pathways, which may involve substantial morbidity, prolonged recovery and extensive scarring. We report successful minimally invasive management via percutaneous endovascular orthotopic inferior vena cava construction in a pediatric patient, thereby obviating the need for surgery and its associated morbidity.

Level of Evidence

Level IV, case study.


IVCA (IVC agenesis) Neocava Interrupted IVC Percutaneous IVC construction 


Compliance with Ethical Standards

Conflict of interest

The authors declare that they have no conflict of interest.

Consent for Publication

For this type of study, consent for publication is not required.

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards. For this type of study, formal consent is not required. Institutional Review Board (IRB) approval is not required for case reports at our institution.

Informed Consent

For this type of study, informed consent is not required.


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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature and the Cardiovascular and Interventional Radiological Society of Europe (CIRSE) 2018

Authors and Affiliations

  • Marc H. Schiffman
    • 1
    Email author
  • Joshua Cornman-Homonoff
    • 2
  • Thomas A. Sos
    • 1
  1. 1.Division of Interventional RadiologyNewYork-Presbyterian Hospital/Weill Cornell Medical CenterNew YorkUSA
  2. 2.Department of RadiologyNewYork-Presbyterian Hospital/Weill Cornell Medical CenterNew YorkUSA

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