CardioVascular and Interventional Radiology

, Volume 30, Issue 3, pp 477–479 | Cite as

Spontaneous Hemothorax in Neurofibromatosis Treated with Percutaneous Embolization

  • Kazunori Arai
  • Junichiro SanadaEmail author
  • Akiko Kurozumi
  • Toshio Watanabe
  • Osamu Matsui


We evaluated the effectiveness of transcatheter arterial coil embolization therapy for the treatment of spontaneous hemothorax followed by aneurysm rupture in neurofibromatosis patients. Three patients were treated for massive hemothorax caused by arterial lesions associated with neurofibromatosis. Bleeding episodes were secondary to ascending cervical artery aneurysm and dissection of vertebral artery in 1 patient, and intercostal artery aneurysm with or without arteriovenous fistula in 2 patients. Patients were treated by transarterial coil embolization combined with chest drainage. In 1 patient, the ruptured ascending cervical artery aneurysm was well embolized but, shortly after the embolization, fatal hemorrhage induced by dissection of the vertebral artery occurred and the patient died. In the other 2 patients, the ruptured intercostal artery aneurysm was well embolized and they were successfully treated and discharged. Transcatheter arterial coil embolization therapy is an effective method for the treatment of spontaneous hemothorax followed by aneurysm rupture in neurofibromatosis patients.


Aneurysm hemothorax Neurofibromatosis Pseudoaneurysm Transcatheter arterial embolization 


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Copyright information

© Springer Science+Business Media, Inc. 2007

Authors and Affiliations

  • Kazunori Arai
    • 1
  • Junichiro Sanada
    • 3
    Email author
  • Akiko Kurozumi
    • 1
  • Toshio Watanabe
    • 2
  • Osamu Matsui
    • 3
  1. 1.Department of RadiologyKurobe City HospitalKurobeJapan
  2. 2.Department Thoracic SurgeryKurobe City HospitalKurobeJapan
  3. 3.Department of RadiologyKanazawa University HospitalKanazawaJapan

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