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International Orthopaedics

, Volume 34, Issue 5, pp 695–702 | Cite as

Surgical management of severe scoliosis with high risk pulmonary dysfunction in Duchenne muscular dystrophy: patient function, quality of life and satisfaction

  • Masashi TakasoEmail author
  • Toshiyuki Nakazawa
  • Takayuki Imura
  • Takamitsu Okada
  • Kensuke Fukushima
  • Masaki Ueno
  • Naonobu Takahira
  • Kazuhisa Takahashi
  • Masashi Yamazaki
  • Seiji Ohtori
  • Hirotsugu Okamoto
  • Toshiyuki Okutomi
  • Makihito Okamoto
  • Takashi Masaki
  • Eijyu Uchinuma
  • Hiroyuki Sakagami
Original Paper

Abstract

In a previous study, the authors reported the clinical and radiological results of Duchenne muscular dystrophy (DMD) scoliosis surgery in 14 patients with a low FVC of <30%. The purpose of this study was to determine if surgery improved function and QOL in these patients. Furthermore, the authors assessed the patients’ and parents’ satisfaction. %FVC increased in all patients after preoperative inspiratory muscle training. Scoliosis surgery in this group of patients presented no increased risk of major complications. All-screw constructions and fusion offered the ability to correct spinal deformity in the coronal and pelvic obliquity initially, intermediate and long-term. All patients were encouraged to continue inspiratory muscle training after surgery. The mean rate of %FVC decline after surgery was 3.6% per year. Most patients and parents believed scoliosis surgery improved their function, sitting balance and quality of life even though patients were at high risk for major complications. Their satisfaction was also high.

Keywords

Pulmonary Function Force Vital Capacity Duchenne Muscular Dystrophy Spinal Muscular Atrophy Spinal Deformity 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag 2010

Authors and Affiliations

  • Masashi Takaso
    • 1
    Email author
  • Toshiyuki Nakazawa
    • 1
  • Takayuki Imura
    • 1
  • Takamitsu Okada
    • 1
  • Kensuke Fukushima
    • 1
  • Masaki Ueno
    • 1
  • Naonobu Takahira
    • 1
  • Kazuhisa Takahashi
    • 2
  • Masashi Yamazaki
    • 2
  • Seiji Ohtori
    • 2
  • Hirotsugu Okamoto
    • 3
  • Toshiyuki Okutomi
    • 3
  • Makihito Okamoto
    • 4
  • Takashi Masaki
    • 4
  • Eijyu Uchinuma
    • 5
  • Hiroyuki Sakagami
    • 6
  1. 1.Department of Orthopaedic Surgery, School of MedicineKitasato UniversitySagamiharaJapan
  2. 2.Department of Orthopaedic Surgery, Graduate School of MedicineChiba UniversityChibaJapan
  3. 3.Department of Anesthesiology, School of MedicineKitasato UniversitySagamiharaJapan
  4. 4.Department of Otorhinolaryngology, School of MedicineKitasato UniversitySagamiharaJapan
  5. 5.Department of Plastic Surgery, School of MedicineKitasato UniversitySagamiharaJapan
  6. 6.Department of Anatomy and Cell Biology, School of MedicineKitasato UniversitySagamiharaJapan

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