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International Orthopaedics

, Volume 29, Issue 4, pp 210–213 | Cite as

Desmoid tumours of the extremities and trunk: a review of the literature

  • Emilios E. PakosEmail author
  • Pericles G. Tsekeris
  • Ann C. Goussia
Review Article

Abstract

Desmoid tumours are rare neoplasms that display local aggressiveness but no propensity to metastasise. They are mainly localized in the abdominal wall, the bowel, and the mesentery or in extra-abdominal sites such as the trunk and the extremities. Surgical resection is the main treatment modality in extremities and trunk, with the optional combination of radiotherapy and/or chemotherapy. However, these tumours have a high propensity for recurrent growth.

Keywords

Familial Adenomatous Polyposis Margin Status Desmoid Tumour Wide Resection Positive Resection Margin 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Résumé

Les tumeurs desmoides sont des néoplasmes rares qui ont un caractère agressif local, mais aucune propension à métastaser. Elles sont principalement localisés dans la paroi abdominale, l’intestin et le mésentère et dans des sites extra-abdominaux tels que le tronc et les extrémités. La résection chirurgicale est la principale modalité du traitement pour les extrémités et le tronc avec la combinaison facultative de radiothérapie et/ou chimiothérapie. Cependant, ils ont une haute tendance à la récidive.

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Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  • Emilios E. Pakos
    • 1
    • 3
    Email author
  • Pericles G. Tsekeris
    • 1
  • Ann C. Goussia
    • 2
  1. 1.Department of Radiation Therapy, University Hospital of Ioannina, School of MedicineUniversity of IoanninaIoanninaGreece
  2. 2.Department of Pathology, University Hospital of Ioannina, School of MedicineUniversity of IoanninaIoanninaGreece
  3. 3.NeohoropouloIoanninaGreece

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