Abdominal Imaging

, Volume 37, Issue 2, pp 261–274

Immunological diseases of the pancreatico-hepatobiliary system: update on etiopathogenesis and cross-sectional imaging findings

  • Deepak Garg
  • Arpit Nagar
  • Shaile Philips
  • Naoki Takahashi
  • Srinivasa R. Prasad
  • Alampady K. Shanbhogue
  • Dushyant V. Sahani


Immunological diseases of the hepatobiliary system and the pancreas include a broad spectrum of disorders that manifest characteristic histopathology/serology and variable clinical features and imaging findings. Recent studies have thrown fresh light on the complex role of genetics and autoimmunity in the pathogenesis and natural history of these diverse disorders that include autoimmune hepatitis, primary biliary cirrhosis, primary sclerosing cholangitis, IgG4-related cholangitis, overlap/outlier syndromes, and autoimmune pancreatitis.

Key words

Autoimmune hepatitis Primary biliary cirrhosis Primary sclerosing cholangitis IgG-4-related disease Computed tomography Magnetic resonance imaging 


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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  • Deepak Garg
    • 1
  • Arpit Nagar
    • 2
  • Shaile Philips
    • 1
  • Naoki Takahashi
    • 3
  • Srinivasa R. Prasad
    • 4
  • Alampady K. Shanbhogue
    • 1
  • Dushyant V. Sahani
    • 5
  1. 1.Department of RadiologyUniversity of Texas Health Science CenterSan AntonioUSA
  2. 2.Department of RadiologyOhio State University Medical CenterColumbusUSA
  3. 3.Department of RadiologyMayo ClinicRochesterUSA
  4. 4.Department of RadiologyUniversity of Texas MD Anderson Cancer CenterHoustonUSA
  5. 5.Department of RadiologyMassachusetts General HospitalBostonUSA

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