Abdominal Imaging

, Volume 29, Issue 4, pp 455–459 | Cite as

Congenital absence of the portal vein associated with focal nodular hyperplasia in the liver in an adult woman

  • A. M. De Gaetano
  • B. Gui
  • G. Macis
  • R. Manfredi
  • C. Di Stasi
Original article


We present a new case of congenital absence of the portal vein and focal nodular hyperplasia in the liver without additional congenital anomalies. Ultrasound, computed tomography, magnetic resonance imaging, and angiography depicted the splenic vein and the superior mesenteric vein joining and entering into the inferior vena cava without passing through the liver. The features of this patient and the 30 previously reported cases are reviewed.


Congenital absence of the portal vein Congenital anomaly of the portal vein Portosystemic shunt Focal nodular hyperplasia 


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Copyright information

© Springer-Verlag New York, Inc. 2004

Authors and Affiliations

  • A. M. De Gaetano
    • 1
  • B. Gui
    • 1
  • G. Macis
    • 1
  • R. Manfredi
    • 1
  • C. Di Stasi
    • 1
  1. 1.Department of Radiology“A. Gemelli” University Hospital, 8, Largo F. Vito, Rome 00168Italy

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