Advertisement

Skeletal Radiology

, Volume 27, Issue 5, pp 278–282 | Cite as

Polyostotic fibrous dysplasia associated with intramuscular myxomas: Mazabraud’s syndrome

  • Carlos Eduardo Lassance Cabral
  • P. Guedes
  • Therezinha Fonseca
  • José Francisco Rezende
  • Luiz Celso Cruz Jr.
  • Julius Smith
CASE REPORT

Abstract 

Mazabraud’s syndrome, though uncommon, is reported increasingly frequently. It represents an entity readily recognisable radiologically on MR imaging. Awareness of the syndrome, particularly when the myxoma is solitary, can prevent misdiagnosis of intramuscular myxomas (especially when large) as malignant mesenchymal tumors containing myxoid tissue. We review the 34 cases previously reported in the literature and include a recent case from our center.

Key words Fibrous dysplasia Soft tissue tumor Intramuscular myxoma MRI Mazabraud’s syndrome 

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

Copyright information

© International Skeletal Society 1998

Authors and Affiliations

  • Carlos Eduardo Lassance Cabral
    • 1
  • P. Guedes
    • 1
  • Therezinha Fonseca
    • 2
  • José Francisco Rezende
    • 3
  • Luiz Celso Cruz Jr.
    • 1
  • Julius Smith
    • 1
  1. 1.Department of Radiology, Instituto Nacional de Câncer (INCA), Praça Cruz Vermelha, 23/3° andar, Centro, Rio de Janeiro/RJ, Brazil 20.230–130BR
  2. 2.Department of Surgical Pathology, Instituto Nacional de Câncer (INCA), Rio de Janeiro, BrazilBR
  3. 3.Department of Surgery, Instituto Nacional de Câncer (INCA), Rio de Janeiro, BrazilBR

Personalised recommendations