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Progressive pseudorheumatoid dysplasia: a report of three cases and a review of radiographic and magnetic resonance imaging findings

  • Christy B. PomeranzEmail author
  • Janet R. Reid
Review Article
  • 29 Downloads

Abstract

Progressive pseudorheumatoid dysplasia (PPD) is a rare disorder of postnatal skeletal and cartilage development that often presents with similar clinical findings to juvenile idiopathic arthritis. Patients with PPD display findings of progressive cartilage loss and secondary osteoarthritis over serial imaging studies and have an absence of elevation of inflammatory markers. Awareness of the imaging features of PPD on radiographs and magnetic resonance imaging (MRI) may be important for early diagnosis and surveillance of the disease.

Keywords

Progressive pseudorheumatoid dysplasia Skeletal dysplasias Juvenile idiopathic arthritis Pediatric radiology Pediatric musculoskeletal imaging Magnetic resonance imaging 

Notes

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Copyright information

© ISS 2019

Authors and Affiliations

  1. 1.Department of RadiologyNew York-Presbyterian Hospital/Weill Cornell MedicineNew YorkUSA
  2. 2.Department of RadiologyThe Children’s Hospital of PhiladelphiaPhiladelphiaUSA

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