Skeletal Radiology

, Volume 42, Issue 10, pp 1447–1450

Late-onset en coup de sabre of the skull

  • Shaun V. Mohan
  • Vinay Nittur
  • Kathryn J. Stevens
Case Report

Abstract

En coup de sabre is a rare subtype of linear scleroderma that characteristically affects the skin, underlying muscle, and bone of the frontoparietal region of the face and scalp. It typically presents in the first two decades of life, and may be associated with focal neurological deficits. We present a case of late-onset en coup de sabre of the frontal bone where the diagnosis was further complicated by a history of breast cancer, prior trauma to the region, and use of topical medication.

Keywords

Frontal linear scleroderma en coup de sabre Linear scleroderma Localized 

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Copyright information

© ISS 2013

Authors and Affiliations

  • Shaun V. Mohan
    • 1
  • Vinay Nittur
    • 2
  • Kathryn J. Stevens
    • 1
  1. 1.Department of RadiologyStanford University School of MedicineStanfordUSA
  2. 2.University of California DavisDavisUSA

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