Skeletal Radiology

, 40:1141 | Cite as

Benign notochordal lesions of the axial skeleton: a review and current appraisal

  • Michael KyriakosEmail author
Special Issue: Jubilee


At the 1996 meeting of the International Skeletal Society, an idea was put forth that there existed symptomatic lesions of the axial skeleton, morphologically different from chordoma, that were consistent with benign notochordal remnants (rests). A review of the embryological basis for this concept is made, along with an analysis of these lesions, termed giant notochordal rests or benign notochordal cell tumors, that have been reported in the intervening 15 years, with a commentary on their relationship, if any, to chordoma.


Giant notochord rest Benign notochord cell tumor Ecchordosis physaliphora Chordoma Axial skeleton Magnetic resonance imaging 



The author gratefully acknowledges Dr. Murali Sundaram for his helpful suggestions in the preparation of this manuscript.


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Copyright information

© ISS 2011

Authors and Affiliations

  1. 1.Division of Surgical PathologyWashington University School of MedicineSt. LouisUSA

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