Skeletal Radiology

, Volume 39, Issue 6, pp 595–600

Primary cutaneous Ewing’s sarcoma/primitive neuroectodermal tumor manifesting numerous small and huge ulcerated masses: its complete remission by chemotherapy and magnetic resonance imaging findings

  • Won-Jong Bahk
  • Eun-Deok Chang
  • Jung Min Bae
  • Kyung-Ah Chun
  • An-Hee Lee
  • Sang-Young Rho
  • Jin Woo Kim
Case Report

Abstract

Extraskeletal Ewing’s sarcoma (ES) and primitive neuroectodermal tumor (PNET) are widely regarded as clinically and histologically identical tumors which consist of small blue round cells. Extraskeletal ESs/PNETs usually occur in the deep soft tissues of the paraspinal region, chest wall, or lower extremities. However, superficially located cases, so-called cutaneous ESs/PNETs, are exceedingly rare, and the vast majority of the reported cases present as a single small mass. We present magnetic resonance imaging (MRI) findings and clinical course of a unique case of primary cutaneous ES/PNET presenting as numerous huge masses with severe ulceration on them.

Keywords

Primary cutaneous Ewing’s sarcoma/primitive neuroectodermal tumor MRI findings Multiple huge masses Clinical outcome 

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Copyright information

© ISS 2010

Authors and Affiliations

  • Won-Jong Bahk
    • 1
  • Eun-Deok Chang
    • 2
  • Jung Min Bae
    • 3
  • Kyung-Ah Chun
    • 4
  • An-Hee Lee
    • 2
  • Sang-Young Rho
    • 5
  • Jin Woo Kim
    • 3
  1. 1.Department of Orthopedic Surgery, Uijeongbu St. Mary’s HospitalThe Catholic University of KoreaUijeongbuKorea
  2. 2.Department of Pathology, Uijeongbu St. Mary’s HospitalThe Catholic University of KoreaUijeongbuKorea
  3. 3.Department of Dermatology, Uijeongbu St. Mary’s HospitalThe Catholic University of KoreaUijeongbuKorea
  4. 4.Department of Radiology, Uijeongbu St. Mary’s HospitalThe Catholic University of KoreaUijeongbuKorea
  5. 5.Department of Hemato-oncology, Uijeongbu St. Mary’s HospitalThe Catholic University of KoreaUijeongbuKorea

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