Skeletal Radiology

, Volume 37, Issue 6, pp 555–558

Lipofibromatosis: report of a rare paediatric soft tissue tumour

  • A. N. Deepti
  • Vrisha Madhuri
  • Noel Malcolm Walter
  • Rekha Aley Cherian
Case Report

Abstract

The clinical, radiological and pathological features of a case of lipofibromatosis, a rare paediatric soft tissue neoplasm, are described. The tumour involved the foot of a male infant and was present at birth. Magnetic resonance imaging showed a lipomatous mass, with splaying of muscles of the sole by lobules of fat. Histopathological examination revealed typical findings of an admixture of mature adipose tissue and fibroblastic elements. The radiological and pathological features helpful in differentiating this entity from other fibro-fatty paediatric soft tissue tumours is discussed, and the relevant literature is briefly reviewed.

Keywords

Infant Foot Lipofibromatosis MRI Fibroblast 

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Copyright information

© ISS 2008

Authors and Affiliations

  • A. N. Deepti
    • 1
  • Vrisha Madhuri
    • 2
  • Noel Malcolm Walter
    • 1
  • Rekha Aley Cherian
    • 3
  1. 1.Department of General PathologyChristian Medical CollegeVelloreIndia
  2. 2.Department of OrthopaedicsChristian Medical CollegeVelloreIndia
  3. 3.Department of RadioDiagnosisChristian Medical CollegeVelloreIndia

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