Pancreatic heterotopia is a rare congenital anomaly more commonly incidentally found in adults. While intra-abdominal cysts found on prenatal imaging are not uncommon, we examine a case of pancreatic heterotopia presenting in an abdominopelvic cyst on prenatal imaging. At birth, the neonate was found to have hypoglycemia unresponsive to treatment that resolved after cyst resection. We will review the etiology, imaging findings and clinical course of this anomaly, which should be considered in the differential diagnosis of newborns presenting with unexplained hypoglycemia.
Auringer ST, Ulmer JL, Sumner TE, Turner CS (1993) Congenital cyst of the pancreas. J Pediatr Surg 28:1570–1571CrossRefGoogle Scholar
Rezvani M, Menias C, Sandrasegaran K et al (2017) Heterotopic pancreas: histopathologic features, imaging findings, and complications. Radiographics 37:484–499CrossRefGoogle Scholar
Cagirici U, Ozbaran M, Veral A, Posacioglu H (2001) Ectopic mediastinal pancreas. Eur J Cardiothorac Surg 19:514–515CrossRefGoogle Scholar
Hussain K, Seppänen M, Näntö-Salonen K et al (2006) The diagnosis of ectopic focal hyperinsulinism of infancy with [18F]-dopa positron emission tomography. J Clin Endocrinol Metab 91:2839–2842CrossRefGoogle Scholar
Cardenas CM, Dominguez I, Campuzano M et al (2009) Malignant insulinoma arising from intrasplenic heterotopic pancreas. JOP 10:321–323PubMedGoogle Scholar