Pediatric Radiology

, Volume 45, Issue 5, pp 763–766 | Cite as

Unusual signal intensity of congenital pulmonary airway malformation on fetal magnetic resonance imaging

  • Keiho OwadaEmail author
  • Osamu Miyazaki
  • Kentaro Matsuoka
  • Haruhiko Sago
  • Shunsuke Nosaka
Case Report


Congenital pulmonary airway malformation (CPAM) is classified into pathologically different types. These types are sometimes distinguishable by fetal lung MRI and are usually observed as higher-signal lesions on T2-weighted images than normal lung. We describe a case of unusual CPAM resembling neoplasms, with a lower signal than is found in normal lung. Histopathology showed a large number of mucogenic cells but found no evidence that could explain this feature on fetal MRI. An unusual low-signal mass associated with a pulmonary cyst in fetal lung on MRI may suggest an unusual type 1 CPAM.


Magnetic resonance imaging Congenital pulmonary airway malformation Mucin Fetus 



We thank Drs. Yasufumi Fuchimoto and Kaori Sato in the Department of Pediatric Surgery at the NCCHD for details of patients’ surgical treatment.

Conflicts of interest



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Copyright information

© Springer-Verlag Berlin Heidelberg 2015

Authors and Affiliations

  • Keiho Owada
    • 1
    Email author
  • Osamu Miyazaki
    • 1
  • Kentaro Matsuoka
    • 2
  • Haruhiko Sago
    • 3
  • Shunsuke Nosaka
    • 1
  1. 1.Department of RadiologyNational Center for Child Health and DevelopmentTokyoJapan
  2. 2.Department of PathologyNational Center for Child Health and DevelopmentTokyoJapan
  3. 3.Department of Perinatal Medicine and Maternal CareNational Center for Child Health and DevelopmentTokyoJapan

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