Congenital pulmonary airway malformation (CPAM) is classified into pathologically different types. These types are sometimes distinguishable by fetal lung MRI and are usually observed as higher-signal lesions on T2-weighted images than normal lung. We describe a case of unusual CPAM resembling neoplasms, with a lower signal than is found in normal lung. Histopathology showed a large number of mucogenic cells but found no evidence that could explain this feature on fetal MRI. An unusual low-signal mass associated with a pulmonary cyst in fetal lung on MRI may suggest an unusual type 1 CPAM.
Magnetic resonance imaging Congenital pulmonary airway malformation Mucin Fetus
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We thank Drs. Yasufumi Fuchimoto and Kaori Sato in the Department of Pediatric Surgery at the NCCHD for details of patients’ surgical treatment.
Conflicts of interest
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