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Pediatric Radiology

, Volume 44, Issue 9, pp 1158–1168 | Cite as

Imaging in congenital pulmonary vein anomalies: the role of computed tomography

  • Kevin Todd Dyer
  • Anthony Marcus Hlavacek
  • Felix Gabriel Meinel
  • Carlo Nicola De Cecco
  • Andrew Douglas McQuiston
  • Uwe Joseph Schoepf
  • Nicholas Peter Pietris
Pictorial Essay

Abstract

Pulmonary venous anomalies comprise a wide spectrum of anatomical variations and their clinical presentations may vary from the relatively benign single partial anomalous pulmonary venous connection (PAPVC) to the critical obstructed total anomalous pulmonary venous connection (TAPVC). We briefly review the common anomalies encountered, while highlighting the utility that computed tomographic angiography (CTA) provides for this spectrum of extracardiac vascular malformations and connections. CTA has established itself as an invaluable imaging modality in these patients. A detailed knowledge of the CTA imaging findings in pulmonary venous anomalies is crucial to guide clinical decision-making in these patients.

Keywords

Pulmonary venous anomalies Computed tomography angiography Total anomalous pulmonary venous connection Partial anomalous pulmonary venous connection Scimitar syndrome 

Notes

Conflicts of interest

U. J. Schoepf is a consultant for and receives research support from Bayer, Bracco, GE, Medrad and Siemens. K. Dyer, A. Hlavacek, F. Meinel, C. De Cecco, A. McQuiston and N. Pietris have no disclosures.

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Copyright information

© Springer-Verlag Berlin Heidelberg 2014

Authors and Affiliations

  • Kevin Todd Dyer
    • 1
  • Anthony Marcus Hlavacek
    • 1
    • 2
  • Felix Gabriel Meinel
    • 1
    • 3
  • Carlo Nicola De Cecco
    • 1
    • 4
  • Andrew Douglas McQuiston
    • 1
  • Uwe Joseph Schoepf
    • 5
    • 1
    • 2
  • Nicholas Peter Pietris
    • 1
    • 2
  1. 1.Department of Radiology and Radiological ScienceMedical University of South CarolinaCharlestonUSA
  2. 2.Division of Cardiology Department of PediatricsMedical University of South CarolinaCharlestonUSA
  3. 3.Institute for Clinical RadiologyLudwig-Maximilians-University HospitalMunichGermany
  4. 4.Department of Radiological Sciences Oncology and PathologyUniversity of Rome “Sapienza” – Polo PontinoLatinaItaly
  5. 5.Division of Cardiology Department of MedicineMedical University of South CarolinaCharlestonUSA

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