Pediatric Radiology

, Volume 44, Issue 4, pp 479–483 | Cite as

Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions

  • Maria A. Calvo-GarciaEmail author
  • Foong-Yen Lim
  • Jerzy Stanek
  • Constance Bitters
  • Beth M. Kline-Fath
Case Report


We present a prenatal case of congenital peribronchial myofibroblastic tumor referred as a congenital pulmonary airway malformation (CPAM) with hydrops and polyhydramnios at 30 weeks’ gestational age. US and fetal MRI findings did not fit with the referral diagnosis, raising the possibility of intrinsic lung tumor. Fetal hydrops worsened and the baby was successfully delivered by ex utero intrapartum treatment (EXIT) to resection at 31 weeks’ gestational age. To the best of our knowledge, this is a unique case of congenital peribronchial myofibroblastic tumor that underwent comprehensive prenatal evaluation and EXIT procedure with good outcome.


Congenital peribronchial myofibroblastic tumor Lung Prenatal diagnosis Fetal MRI Sonography 


Conflicts of interest



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Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Maria A. Calvo-Garcia
    • 1
    Email author
  • Foong-Yen Lim
    • 2
  • Jerzy Stanek
    • 3
  • Constance Bitters
    • 1
  • Beth M. Kline-Fath
    • 1
  1. 1.Department of Radiology, MLC 5031Cincinnati Children’s Hospital Medical CenterCincinnatiUSA
  2. 2.Department of Pediatric Surgery and Fetal Care Center of CincinnatiCincinnati Children’s Hospital Medical CenterCincinnatiUSA
  3. 3.Department of PathologyCincinnati Children’s Hospital Medical CenterCincinnatiUSA

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