Spinal cord signal abnormality resulting from alterations in cerebrospinal fluid flow at the craniocervical junction has been termed a presyrinx state. This condition has been described in the adult literature in association with a variety of conditions that cause obstruction to normal cerebrospinal fluid flow. We present a case of presyrinx in a child in the setting of acquired Chiari I malformation caused by lumboperitoneal overshunting. Awareness of the potentially reversible nature of this condition might allow for intervention before irreversible neurological damage has occurred.
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Nixon, J.N., Stanescu, L.A. & Weinberger, E. Presyrinx in a child with acquired Chiari I malformation. Pediatr Radiol 43, 506–511 (2013). https://doi.org/10.1007/s00247-012-2488-x
- Chiari I malformation